PAPVC

partial anomalous pulmonary venous connection(English)

  • isolated type has been implicated as a cause of pulmonary arterial hypertension. However, this condition is often overlooked in the diagnostic work up of patients with PH. Found in around 0.4–0.7 % of autopsies. In most cases the anomalous venous connection involves the right pulmonary veins that drain into the superior vena cava or the right atrium. Anomalous pulmonary veins less frequently drain into the inferior vena cava, innominate vein or the coronary sinus. These anomalous veins are frequently associated with other congenital heart anomalies, predominantly atrial septal defects. An anomalous pulmonary venous connection occurs in approximately 10–15% of ostium secundum ASD and 85 % of patients with sinus venosus ASD. Adversely affects the cardio-pulmonary physiology by presenting as a left–to-right shunt, aggravated by frequent co-existent atrial septal defects
  • ASD, PAH, PH, RA, SVC
  • Congenital disorders, Cardiology, Pulmonology
  • https://doi.org…43.2012.02180.x